冨田 周介¹, 赤阪 隆史¹, 高鍬 博¹, 平佐 昌弘¹, 伊吹 康良¹, 工藤 正俊¹, 新垣 光彌¹, 藤堂 彰男¹, 藤本 敏明², 久米 正紀³, 細川 友舶³, 水間 和郎³

Shusuke TOMITA¹, Takashi AKASAKA¹, Hiroshi TAKAKUWA¹, Akihiro HIRASA¹, Yasuyoshi IBUKI¹, Masanori KUBO¹, Mitsuya SHINGAKI¹, Akio TODO¹, Toshiaki FUJIMOTO², Masanori KIME³, Tomohiro HOSOKAWA³, Kazuo MIZUMA³

¹神戸市立中央市民病院内科, ²神戸市立中央市民病院中央検査室, ³水間医院

¹Department of Internal Medicine, Kobe Central Municipal Hospital, ²Central Laboratory, Kobe Central Municipal Hospital, ³Mizuma Clinic

キーワード : ultrasonography, Caroli's disease

Three patients with Caroli's disease in siblings were presented. Caroli's disease was suspected by ultrasound, and then confirmed by hepato-biliary scintigrams (ggm TC-PI). With ultrasound, multiple spindle-shaped cystic lesions with folds were found in the liver of all three patients. In two, a tubular structure (the intrahepatic bile duct) communicating with every cystic lesions was recognized. In one patient, a stone within the cystic lesion was visualized. Furthermore, in two cases, medullary cysts of the kidney were shown. Hepato-biliary scientigrams demonstrated multiple dilatations of the intrahepatic bile duct at excretory phase in all.
We conclude that ultrasonography can diagnose Caroli's disease by the shape of the cystic lesions and the communication between the cysts and the bile ducts. If necessary, it is confirmed by hepato-biliary scintigram.